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E70 Disorders of aromatic amino-acid metabolism

ICD-10-CM category E70 sits in Chapter 4 (Endocrine, nutritional and metabolic diseases, E00-E89). It contains 26 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

E70.2 Disorders of tyrosine metabolismE70.3 AlbinismE70.31 Ocular albinismE70.32 Oculocutaneous albinismE70.33 Albinism with hematologic abnormalityE70.4 Disorders of histidine metabolismE70.8 Other disorders of aromatic amino-acid metabolism

Billable codes in E70

CodeDescription
E70.0Classical phenylketonuria
E70.1Other hyperphenylalaninemias
E70.20Disorder of tyrosine metabolism, unspecified
E70.21Tyrosinemia
E70.29Other disorders of tyrosine metabolism
E70.30Albinism, unspecified
E70.310X-linked ocular albinism
E70.311Autosomal recessive ocular albinism
E70.318Other ocular albinism
E70.319Ocular albinism, unspecified
E70.320Tyrosinase negative oculocutaneous albinism
E70.321Tyrosinase positive oculocutaneous albinism
E70.328Other oculocutaneous albinism
E70.329Oculocutaneous albinism, unspecified
E70.330Chediak-Higashi syndrome
E70.331Hermansky-Pudlak syndrome
E70.338Other albinism with hematologic abnormality
E70.339Albinism with hematologic abnormality, unspecified
E70.39Other specified albinism
E70.40Disorders of histidine metabolism, unspecified
E70.41Histidinemia
E70.49Other disorders of histidine metabolism
E70.5Disorders of tryptophan metabolism
E70.81Aromatic L-amino acid decarboxylase deficiency
E70.89Other disorders of aromatic amino-acid metabolism
E70.9Disorder of aromatic amino-acid metabolism, unspecified

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